Reninoma is a rare kidney tumor that causes high blood pressure. The article describes the case of a patient with ten-year hypertension, in whom the diagnosis was confirmed by bilateral sampling of the renal veins and pathological examination. The patient underwent radiofrequency ablation of the tumor and later partial nephrectomy, after which the blood pressure normalized. An analysis of 62 cases of reninoma in China from 2016 to May 2025 revealed three types: 44 typical reninomas, 16 atypical reninomas (with hypertension and normal potassium levels), and 2 nonfunctioning reninomas. According to the article, young women with high renin and aldosterone should raise the suspicion of reninoma. Diagnosis requires a combination of clinical picture, imaging findings and pathological characteristics. Curative treatment can be achieved by tumor resection with preservation of renal units.